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Start free with EleplanMalignant Sertoli-Leydig cell tumor of the ovary
ORPHA:99916Disease
Also called Androblastoma · Arrhenoblastoma · Ovarian Sertoli-Leydig cell cancer · Ovarian malignant Sertoli-Leydig cell tumor · Virilizing ovarian tumor
What it is
A rare malignant sex cord stromal tumor of ovary occuring typically in young women and characterized by manifestations of androgen excess (hirsutism, hair loss, amenorrhea, or oligomenorrhea), when functional.
Key facts
- Prevalence
- <1 / 1 000 000 (annual incidence, Europe)
- Age of onset
- Adolescent, Adult, Childhood, Elderly
- Classified as
- Disease
Recorded for the broader condition
- Inheritance
- Not applicableMalignant sex cord stromal tumor of ovary
Orphanet records these for the broader condition rather than for this specific form. They are a starting point, not a figure for this subtype — subtypes often differ, and some are defined by being rarer than the condition they sit under.
Prevalence figures describe populations, not individuals, and are often estimates from a single study. Where the figure is an incidence or a birth prevalence, it says so.
Gene
ICD-10 codes
ICD-10 has no distinct code for most rare diseases, so many are filed under the nearest available one. A shared code identifies the group, not this disease — the ORPHAcode above is what identifies it.
Related health topics
Reached through the ICD-10 categories this disease is filed under, so these describe the broader group rather than this disease specifically.
Cross-references
Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.
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