Idiopathic ventricular fibrillation

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Idiopathic ventricular fibrillation

ORPHA:228140Disease

What it is

A rare, genetic, cardiac rhythm disease characterized by ventricular fibrillation in the absence of any structural or functional heart disease, or known repolarization abnormalities. The presence of J waves is associated with a higher risk of nocturnal ventricular fibrillation events and a higher risk of recurrence.

Key facts

Age of onset
All ages
Inheritance
Autosomal dominant, Not applicable
Classified as
Disease

Genes

DPP6Disease-causing germline mutation(s)
SCN5ADisease-causing germline mutation(s)

ICD-10 codes

I49.0filed under a broader ICD-10 category

Related health topics

Reached through the ICD-10 categories this disease is filed under, so these describe the broader group rather than this disease specifically.

Cross-references

GARD 4227OMIM 603829OMIM 612956UMLS C4510132

Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.

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