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Start free with EleplanIdiopathic steroid-sensitive nephrotic syndrome
ORPHA:69061Clinical syndrome
What it is
A rare primary glomerulopathy of unknown cause characterized by edema, nephrotic-range proteinuria and hypoalbuminemia that responds to standard prednisone treatment within 4-6 weeks.
Key facts
- Age of onset
- All ages
- Inheritance
- Unknown
- Classified as
- Clinical syndrome
Signs and symptoms
These ranges are how often a sign appears across everyone diagnosed, not a prediction for one person — most people have some of these and not others. Orphanet also records findings that are specifically absent in this disease; those are in the data but not listed here.
ICD-10 codes
Cross-references
Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.
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