CHD8 overgrowth syndrome

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CHD8 overgrowth syndrome

ORPHA:642675Disease

Also called CHD8-related intellectual disability-autism-macrocephaly-tall stature syndrome · Chromodomain helicase DNA binding protein 8 overgrowth syndrome

What it is

A rare multiple congenital anomalies/dysmorphic syndrome characterized by mild to moderate intellectual disability, autism spectrum phenotype, macrocephaly, tall stature, gastrointestinal problems (including recurrent constipation), distinctive facial features (including wide-set eyes with down-slanted palpebral fissure, broad nose with full nasal tip, pointed chin and broad forehead with prominent supraorbital ridge) and sleep problems. Other clinical manifestations include anxiety problems, attention problems, impaired social interactions and seizures.

Key facts

Prevalence
<1 / 1 000 000
Age of onset
No data available
Inheritance
Autosomal dominant
Classified as
Disease

Prevalence figures describe populations, not individuals, and are often estimates from a single study. Where the figure is an incidence or a birth prevalence, it says so.

Gene

CHD8Disease-causing germline mutation(s) (loss of function)

ICD-10 codes

Q87.3filed under a broader ICD-10 category — shared with 40 other rare diseases

ICD-10 has no distinct code for most rare diseases, so many are filed under the nearest available one. A shared code identifies the group, not this disease — the ORPHAcode above is what identifies it.

Related health topics

Reached through the ICD-10 categories this disease is filed under, so these describe the broader group rather than this disease specifically.

Cross-references

MONDO 0014017OMIM 615032UMLS C5816801

Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.

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