Q89.81

Billable

Kabuki syndrome

Q89.81 is the ICD-10-CM code for Kabuki syndrome. It is a billable, specific code valid for reimbursement.

Status
Billable
Chapter
Q00-Q99
Parent
Q89.8
Edition
FY2026

Q00-Q99 Congenital malformations, deformations and chromosomal abnormalities

Includes

  • Kabuki syndrome, type 1, due to KMT2D mutation
  • Kabuki syndrome, type 2, due to KDM6A mutation
  • Niikawa-Kuroki syndrome

Frequently asked questions

What is ICD-10 code Q89.81?
Q89.81 is the ICD-10-CM code for "Kabuki syndrome". It falls under Q00-Q99 Congenital malformations, deformations and chromosomal abnormalities.
Is Q89.81 a billable code?
Yes — Q89.81 is a billable, specific ICD-10-CM code valid for reimbursement.

Source: CMS ICD-10-CM FY2026. For informational purposes only — not medical advice. See our medical disclaimer.

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