H49.81
Non-billableKearns-Sayre syndrome
H49.81 is the ICD-10-CM code for Kearns-Sayre syndrome. It is a non-billable category code — use a more specific child code such as H49.811 for billing.
H00-H59 Diseases of the eye and adnexa
Includes
- •Progressive external ophthalmoplegia with pigmentary retinopathy
Notes
- •, if applicable, other manifestations, such as:
- •heart block (I45.9)
Frequently asked questions
Source: CMS ICD-10-CM FY2026. For informational purposes only — not medical advice. See our medical disclaimer.
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