E88.43

Billable

Disorders of mitochondrial tRNA synthetases

E88.43 is the ICD-10-CM code for Disorders of mitochondrial tRNA synthetases. It is a billable, specific code valid for reimbursement.

Status
Billable
Chapter
E00-E89
Parent
E88.4
Edition
FY2026

E00-E89 Endocrine, nutritional and metabolic diseases

Includes

  • ARS2-related mitochondrial disorders
  • LBSL
  • Leukoencephalopathy with brainstem - spinal cord involvement - lactate elevation
  • Leukoencephalopathy with thalamus - brainstem involvement - high lactate
  • LTBL
  • Mitochondrial aminoacyl-tRNA synthetase disorders

Notes

  • , if applicable, associated condition such as:
  • leukoencephalopathy (G93.49)

Frequently asked questions

What is ICD-10 code E88.43?
E88.43 is the ICD-10-CM code for "Disorders of mitochondrial tRNA synthetases". It falls under E00-E89 Endocrine, nutritional and metabolic diseases.
Is E88.43 a billable code?
Yes — E88.43 is a billable, specific ICD-10-CM code valid for reimbursement.

Source: CMS ICD-10-CM FY2026. For informational purposes only — not medical advice. See our medical disclaimer.

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