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E88.4

Non-billable

Mitochondrial metabolism disorders

E88.4 is the ICD-10-CM code for Mitochondrial metabolism disorders. It is a non-billable category code — use a more specific child code such as E88.40 for billing.

Status
Header (non-billable)
Chapter
E00-E89
Parent
E88
Subcodes
5
Edition
FY2026

E00-E89 Endocrine, nutritional and metabolic diseases

Excludes1 — not coded here

  • •disorders of pyruvate metabolism (E74.4)
  • •Kearns-Sayre syndrome (H49.81)
  • •Leber's disease (H47.22)
  • •Leigh's encephalopathy (G31.82)
  • •Mitochondrial myopathy, NEC (G71.3)
  • •Reye's syndrome (G93.7)

Frequently asked questions

What is ICD-10 code E88.4?
E88.4 is the ICD-10-CM code for "Mitochondrial metabolism disorders". It falls under E00-E89 Endocrine, nutritional and metabolic diseases.
Is E88.4 a billable code?
No — E88.4 is a non-billable header code. Use a more specific child code (such as E88.40) for billing.
What are the subcodes of E88.4?
E88.4 has 5 more specific child codes, including E88.40, E88.41, E88.42.
What is excluded from E88.4?
Excludes1 (not coded here): disorders of pyruvate metabolism (E74.4); Kearns-Sayre syndrome (H49.81); Leber's disease (H47.22); Leigh's encephalopathy (G31.82).

Source: CMS ICD-10-CM FY2026. For informational purposes only — not medical advice. See our medical disclaimer.

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