E75.241
BillableNiemann-Pick disease type B
E75.241 is the ICD-10-CM code for Niemann-Pick disease type B. It is a billable, specific code valid for reimbursement.
E00-E89 Endocrine, nutritional and metabolic diseases
Includes
- •Acid sphingomyelinase deficiency type B (ASMD type B)
- •Chronic visceral acid sphingomyelinase deficiency
Frequently asked questions
Source: CMS ICD-10-CM FY2026. For informational purposes only — not medical advice. See our medical disclaimer.
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