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BillableDisorders of pyruvate metabolism and gluconeogenesis
E74.4 is the ICD-10-CM code for Disorders of pyruvate metabolism and gluconeogenesis. It is a billable, specific code valid for reimbursement.
E00-E89 Endocrine, nutritional and metabolic diseases
What this means — in plain language
MedlinePlus · NIHMetabolism is the process your body uses to get or make energy from the food you eat. Food is made up of proteins, carbohydrates, and fats. Chemicals in your digestive system break the food parts down into sugars and acids, your body's fuel. Your body can use this fuel right away, or it can store the energy in your body tissues, such as your liver, muscles, and body fat. A metabolic disorder occurs when abnormal…
Read more about Metabolic Disorders at MedlinePlus ↗Source: U.S. National Library of Medicine (MedlinePlus). Informational only — not medical advice.
Includes
- •Deficiency of phosphoenolpyruvate carboxykinase
- •Deficiency of pyruvate carboxylase
- •Deficiency of pyruvate dehydrogenase
Excludes1 — not coded here
Medications indicated for this condition
FDA labelingDrugs whose FDA labeling lists this condition's category among its indications. Informational only — not a treatment recommendation or medical advice.
Conditions mapped to this code
MedlinePlus · NIHPlain-language health-topic references grounded in MedlinePlus (NIH/NLM).
14 rare diseases filed under this code
Orphanet · INSERMICD-10 has no distinct code for most rare diseases, so many are filed under the nearest available one. This code is shared — showing 12 of 14.
Orphadata Science: Free access data from Orphanet. © INSERM 1999.
Frequently asked questions
Source: CMS ICD-10-CM FY2026. For informational purposes only — not medical advice. See our medical disclaimer.
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