E71.0
BillableMaple-syrup-urine disease
E71.0 is the ICD-10-CM code for Maple-syrup-urine disease. It is a billable, specific code valid for reimbursement.
E00-E89 Endocrine, nutritional and metabolic diseases
No additional coding notes for this code.
Frequently asked questions
Source: CMS ICD-10-CM FY2026. For informational purposes only — not medical advice. See our medical disclaimer.
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